A cluster of cystic fibrosis mutations in exon 17b of the CFTR gene : a site for rare mutationsMERCIER, B; LISSENS, W; SAVOV, A et al.Journal of medical genetics. 1994, Vol 31, Num 9, pp 731-734, issn 0022-2593Article

Effects of pyrophosphate and nucleotide analogs suggest a role for ATP hydrolysis in cystic fibrosis transmembrane regulator channel gatingGUNDERSON, K. L; KOPITO, R. R.The Journal of biological chemistry (Print). 1994, Vol 269, Num 30, pp 19349-19353, issn 0021-9258Article

Partial purification of the cystic fibrosis transmembrane conductance regulatorOSTEDGAARD, L. S; WELSH, M. J.The Journal of biological chemistry (Print). 1992, Vol 267, Num 36, pp 26142-26149, issn 0021-9258Article

Cystic fibrosis gene and protein expression during fetal lung developmentMCGRATH, S. A; ANJULI BASU; ZEITLIN, P. L et al.American journal of respiratory cell and molecular biology. 1993, Vol 8, Num 2, pp 201-208, issn 1044-1549Article

Regulation of the cystic fibrosis transmembrane conductance regulator Cl^- channel by specific protein kinases and protein phosphatasesBERGER, H. A; TRAVIS, S. M; WELSH, M. J et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 3, pp 2037-2047, issn 0021-9258Article

Mechanism of inhibition of cAMP-dependent epithelial chloride secretion by phorbol estersBEN-QUAN SHEN; BARTHELSON, R. A; SKACH, W et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 25, pp 19070-19075, issn 0021-9258Article

Nucleoside triphosphates are required to open the CFTR chloride channelANDERSON, M. P; BERGER, H. A; RICH, D. P et al.Cell (Cambridge). 1991, Vol 67, Num 4, pp 775-784, issn 0092-8674Article

Mapping of cystic fibrosis transmembrane conductance regulator membrane topology by glycosylation site insertionXIU-BAO CHANG; YUE-XIAN HOU; JENSEN, T. J et al.The Journal of biological chemistry (Print). 1994, Vol 269, Num 28, pp 18572-18575, issn 0021-9258Article

Expression of the cystic fibrosis transmembrane conductance regulator from a novel adeno-associated virus promoterFLOTTE, T. R; AFIONE, S. A; SOLOW, R et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 5, pp 3781-3790, issn 0021-9258Article

Identification of the major phosphorylation domain of murine mdr1b P-glycoprotein : analysis of the protein kinase A and protein kinase C phosphorylation sitesORR, G. A; HAN, E. K.-H; BROWNE, P. C et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 33, pp 25054-25062, issn 0021-9258Article

Bacterial periplasmic permeases as model systems for the superfamily of traffic ATPases, including the multidrug resistance protein and the cystic fibrosis transmembrane conductance regulatorFERRO-LUZZI AMES, G.International review of cytology. 1992, Vol 137A, pp 1-35, issn 0074-7696Article

Activation of the cystic fibrosis transmembrane conductance regulator by cGMP in the human colonic cancer cell line, caco-2XIAO-YING TIEN; BRASITUS, T. A; KAETZEL, M. A et al.The Journal of biological chemistry (Print). 1994, Vol 269, Num 1, pp 51-54, issn 0021-9258Article

Pyridine nucleotide redox potential modulates cystic fibrosis transmembrane conductance regulator Cl^- conductanceSTUTTS, M. J; GABRIEL, S. E; PRICE, E. M et al.The Journal of biological chemistry (Print). 1994, Vol 269, Num 12, pp 8667-8674, issn 0021-9258Article

The cystic fibrosis transmembrane conductance regulator : overexpression, purification, and characterization of wild type and ΔF508 mutant forms of the first nucleotide binding fold in fusion with the maltose-binding proteinYOUNG HEE KO; THOMAS, P. J; DELANNOY, M. R et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 32, pp 24330-24338, issn 0021-9258Article

CFTR : development of high- affinity antibodies and localization in sweat glandCOHN, J. A; MELHUS, O; PAGE, L. J et al.Biochemical and biophysical research communications (Print). 1991, Vol 181, Num 1, pp 36-43, issn 0006-291XArticle

Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sitesXIU-BAO CHANG; TABCHARANI, J. A; YUE-XIAN HOU et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 15, pp 11304-11311, issn 0021-9258Article

Protein kinase C mediates down-regulation of cystic fibrosis transmenbrane conductance regulator levels in epithelial cellsBREUER, W; GLICKSTEIN, H; KARTNER, N et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 19, pp 13935-13939, issn 0021-9258Article

Biochemical characterization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis epithalial cellsSARKADI, B; BAUZON, D; HUCKLE, W. R et al.The Journal of biological chemistry (Print). 1992, Vol 267, Num 3, pp 2087-2095, issn 0021-9258Article

Ultrastructural localization of variant forms of cystic fibrosis transmembrane conductance regulator in human bronchial epithelia of xenograftsYIPING YANG; ENGELHARDT, J. F; WILSON, J. M et al.American journal of respiratory cell and molecular biology. 1994, Vol 11, Num 1, pp 7-15, issn 1044-1549Article

Characterization of the cystic fibrosis transmembrane conductance regulator promoter region : chromatin context and tissue-specificityKOH, J; SFERRA, T. J; COLLINS, F. S et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 21, pp 15912-15921, issn 0021-9258Article

Interaction of nucleotides with membrane-associated cystic fibrosis transmembrane conductance regulatorTRAVIS, S. M; CARSON, M. R; RIES, D. R et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 21, pp 15336-15339, issn 0021-9258Article

The δF508 mutation decreases the stability of cystic fibrosis transmembrane conductance regulator in the plasma membrane : determination of functional half-lives on transfected cellsLUKACS, G. L; XIU-BAO CHANG; BEAR, C et al.The Journal of biological chemistry (Print). 1993, Vol 268, Num 29, pp 21592-21598, issn 0021-9258Article

Aberrant CFTR-dependent HCO₃^- transport in mutations associated with cystic fibrosisJOO YOUNG CHOL; MUALLEM, Danlella; KISELYOV, Kirill et al.Nature (London). 2001, Vol 410, Num 6824, pp 94-97, issn 0028-0836Article

Cystic fibrosis and the pancreas: Recent scientific advancesNOUSIA-ARVANITAKIS, S.Journal of clinical gastroenterology. 1999, Vol 29, Num 2, pp 138-142, issn 0192-0790Article

Analysis of the CFTR gene confirms the high genetic heterogeneity of the Spanish population : 43 mutations account for only 78% of CF chromosomesCHILLON, M; CASALS, T; GIMENEZ, J et al.Human genetics. 1994, Vol 93, Num 4, pp 447-451, issn 0340-6717Article